The baby who had placental adherence between fetal site of placenta and omphalocele sac was presented. A 21 years old woman, gravida 2, parity 0, abortion 1 was admitted to the Selçuk University, Medical Faculty of Meram, Department of Obstetrics and Gynecologic, because of beginning the labor. Omphalocele was seen with ultrasonographie. Cesarean section was preferred according to desire of the family. A placental adherence between fetal site of placenta and omphalocele sac was detected during cesarean section. This adherence was divided and the baby was delivered. But baby died because of major cardiac anomalies. Anomalies such as omphalocel may be together with adherence between omphalocele sac and placenta or membranes.