A 26-year-old man was admitted to our clinic with approximately 8 years history of hearing loss on the right side. The pathological findings were not found in the neuro-otological examination. Severity sensorinoral hearing loss (SNHL) was determined on the pure tone audiometry. The magnetic resonance imaging (MRI) and computed tomography (CT) were shown that the lipomatous lesion involved right cochlea, semicircular canal and internal auditorium canal. Intralabyrinthine lipoma was diagnosed via fat suppression techniques with MRI on T1-weighted images. The patient followed with MRI because he had just SNHL and the lesion minimal involved internal auditory canal.