CASE REPORT
Telescopic Aortic Arch: A New Entity in Marfan Syndrome
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1
Mustafa Kemal University Medical Faculty
Department of Forensic Medicine, Hatay,
Turkey
2
Dicle University Faculty of Medicine Department
of Forensic Medicine, Diyarbakır,
Turkey
3
Mustafa Kemal University Medical Faculty
Department of Anatomy, Hatay, Turkey
Publication date: 2011-07-11
Corresponding author
Ramazan Akçan
Hacettepe Üniversitesi Tıp Fakültesi, Adli
Tıp Anabilim Dalı, Ankara, Türkiye
Eur J Gen Med 2011;8(3):236-239
KEYWORDS
ABSTRACT
Telescopic aortic arch is a consequence of aortic dissection in Marfan’s
syndrome, which has not been reported previously. This paper presents
the first case of telescopic aortic arch secondary to chronic aortic
dissection, as an incidental finding of a forensic autopsy. Here we
present a sudden death of a 20 years old male due to cardiac tamponade
sourcing from the rupture of ascending aorta. At autopsy, there
was a haemopericardium of 800 cc, which comprised blood and clot.
The ascending thoracic aorta was dilated and a 1.2 cm ragged linear
complete rupture was noticed on the medial side of the front wall of
ascending aorta. Examination of aorta showed a second/inner aortic
arch just as a tube lying inside the aortic arch. The inner aortic arch
was arrised 2.5 cm above aortic valves and lasted at the beginning
of the descending aorta. It was 10 cm in length with a lumen 2 cm
in diameter and was associated with truncus brachiosephalicus, left
common carotid, and left subclavian arteries.