To present a rare case which was resembling ovarian sex cord tumours. A 37 year old woman who had vaginal bleeding for three months was admitted to our clinic. An intracavitary mass was detected after the saline infusion sonography. The patient had operative hysteroscopy. A submucosal mass was resected with hysterescopic knife and resectoscope. According to pathology report, the tumour was diagnosed as uterine tumour resembling ovarian sex cord tumour (UTROSCT) infiltrating half of the myometrial wall. Then a thorough systemic evaluation was performed in order to detect any metastatic lesions. After evaluation of all systems, total abdominal hysterectomy and pelvic-paraaortic lymph node sampling was performed. All the diagnostic and therapeutic procedures were done in our clinic. There are no common consensus for approaching to these patients, these tumours are so rare and clinical features are so variable. Extensive studies must be performed about these tumours.